Dentinogenesis Imperfecta

Dentin, Hereditary Opalescent; Dentinogenesis Imperfectas; Dentins, Hereditary Opalescent; Hereditary Opalescent Dentins; Imperfecta, Dentinogenesis; Imperfectas, Dentinogenesis; Opalescent Dentin, Hereditary; Opalescent Dentins, Hereditary
An autosomal dominant disorder of tooth development characterized by opalescent dentin resulting in discoloration of the teeth, ranging from dusky blue to brownish. The dentin is poorly formed with an abnormally low mineral content; the pulp canal is obliterated, but the enamel is normal. The teeth usually wear down rapidly, leaving short, brown stumps. (Dorland, 27th ed)