G(M1) Ganglioside

GM1a Monosialoganglioside; Ceramide, Monosialosyl Tetraglycosyl; Monosialoganglioside, GM1a; Tetraglycosyl Ceramide, Monosialosyl
A specific monosialoganglioside that accumulates abnormally within the nervous system due to a deficiency of GM1-b-galactosidase, resulting in GM1 gangliosidosis.