G(M2) Activator Protein

GM(2) Activating Protein; GM2 Activator Protein; Hexosaminidase Activator; Activator Protein, GM2
An essential cofactor for the degradation of G(M2)GANGLIOSIDE by lysosomal BETA-N-ACETYLHEXOSAMINIDASE. Genetic mutations resulting in loss of G(M2) activator protein are one of the causes of TAY-SACHS DISEASE, AB VARIANT.