G(M2) Ganglioside

Ganglioside GM2; GM2, Ganglioside; Ganglioside, Tay-Sachs Disease; Tay Sachs Disease Ganglioside
A glycosphingolipid that accumulates due to a deficiency of hexosaminidase A or B (BETA-N-ACETYLHEXOSAMINIDASE), or GM2 activator protein, resulting in GANGLIOSIDOSES, heredity metabolic disorders that include TAY-SACHS DISEASE and SANDHOFF DISEASE.