Histiocytosis, Langerhans-Cell |
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| Hand-Schueller-Christian Syndrome; Histiocytosis, Generalized; Histiocytosis-X; Letterer-Siwe Disease; Schueller-Christian Disease; Disease, Letterer-Siwe; Disease, Schueller-Christian; Generalized Histiocytoses; Generalized Histiocytosis | |
| Group of disorders characterized by monoclonal proliferation of CD1+ HISTIOCYTES. The demonstration of the LANGERHANS CELLS Birbeck granules is the gold standard of the phenotype. EOSINOPHILIC GRANULOMA makes up 60-80% of all the cases. | |