Isovaleryl-CoA Dehydrogenase |
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| Isovaleryl CoA Dehydrogenase; Isovaleryl-Coenzyme A Dehydrogenase; A Dehydrogenase, Isovaleryl-Coenzyme; CoA Dehydrogenase, Isovaleryl; Dehydrogenase, Isovaleryl CoA; Dehydrogenase, Isovaleryl-CoA; Dehydrogenase, Isovaleryl-Coenzyme A | |
| A mitochondrial flavoprotein, this enzyme catalyzes the oxidation of 3-methylbutanoyl-CoA to 3-methylbut-2-enoyl-CoA using FAD as a cofactor. Defects in the enzyme, is associated with isovaleric acidemia (IVA). | |