Neurilemmoma

Malignant Neurilemoma; Neurilemoma; Malignant Neurilemomas; Neurilemmomas; Neurilemmosarcomas; Neurilemoma, Malignant; Neurilemomas; Neurilemomas, Malignant; Neurinomas; Plexiform Schwannomatoses; Plexiform Schwannomatosis; Schwannomas
A neoplasm that arises from SCHWANN CELLS of the cranial, peripheral, and autonomic nerves. Clinically, these tumors may present as a cranial neuropathy, abdominal or soft tissue mass, intracranial lesion, or with spinal cord compression. Histologically, these tumors are encapsulated, highly vascular, and composed of a homogenous pattern of biphasic fusiform-shaped cells that may have a palisaded appearance. (From DeVita Jr et al., Cancer: Principles and Practice of Oncology, 5th ed, pp964-5)