Ornithine Carbamoyltransferase |
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| Ornithine Carbamylphosphate Transferase; Carbamoyltransferase, Ornithine; Carbamylphosphate Transferase, Ornithine; Transcarbamylase, Ornithine; Transferase, Ornithine Carbamylphosphate | |
| A urea cycle enzyme that catalyzes the formation of orthophosphate and L-citrulline (CITRULLINE) from CARBAMOYL PHOSPHATE and L-ornithine (ORNITHINE). Deficiency of this enzyme may be transmitted as an X-linked trait. EC 2.1.3.3. | |