Sarcosine Dehydrogenase

Monomethylglycine Dehydrogenase; Sarcosine N-Demethylase; Dehydrogenase, Monomethylglycine; Dehydrogenase, Sarcosine; N-Demethylase, Sarcosine; Sarcosine N Demethylase
A LIVER mitochondrial matrix flavoenzyme that catalyzes the oxidation of SARCOSINE to GLYCINE and FORMALDEHYDE. Mutation in the enzyme causes sarcosinemia, a rare autosomal metabolic defect characterized by elevated levels of SARCOSINE in BLOOD and URINE.