gamma-Butyrobetaine Dioxygenase

4-Trimethylaminobutyrate, 2-Oxoglutarate Oxygen Oxidoreductase (3-Hydroxylating); Butyrobetaine Hydroxylase; Trimethylaminobutyrate Hydroxylase; gamma-Butyrobetaine Hydroxylase; gamma-Butyrobetaine, 2-Oxoglutarate Dioxygenase
An enzyme that catalyzes the HYDROXYLATION of gamma-butyrobetaine to L-CARNITINE. It is the last enzyme in the biosynthetic pathway of L-CARNITINE and is dependent on alpha-ketoglutarate; IRON; ASCORBIC ACID; and OXYGEN.